Sickle cell disease (SCD), or sickle cell anemia (SCA) is a group of hereditary blood disorders characterized by an abnormality in the oxygen-carrying hemoglobin molecule in red blood cells. As an outpatient department nurse, she is a seasoned nurse in providing health teachings to her patients making her also an excellent study guide writer for student nurses. Major Complications of Sickle Cell Disease and Nursing Implications; Complication. On the basis of the knowledge of the inheritance of the sickle cell gene, the nurse expects the patient to be of what descent? No time limit for this exam. It is estimated that there are between 12,500 and 15,000 people with sickle cell … B. Adequate intake is necessary to provide for mobilization of secretions and prevent hyperviscosity of blood occlusion. It must be treated with medications that are safe to use during pregnancy. Symptoms and duration of pain, dyspnoea, fever, pallor and lethargy ; … Participate in ADLs without weakness and fatigue. Findings demonstrated that it is … C. Middle Eastern. A: The sickle hemoglobin (HbS) gene is inherited in people of African descent. Monitor vital signs and note changes in cardiac rhythm. B. Indian. Practice Mode: This is an interactive version of the Text Mode. Nurseslabs.com is an education and nursing lifestyle website geared towards helping student nurses and registered nurses with knowledge for the progression and empowerment of their nursing careers. Therapeutic Communication Techniques Quiz. … Your doctor might recommend a folic acid supplement. The most common forms of SCDs are: homozygous hemoglobin SS disease (sickle cell anemia), hemoglobin SC disease, and sickle [beta]-thalassemia. Transcranial Doppler (TCD) Used to assess intracranial vascular flow and detect the risk for cerebrovascular accident (CVA). Most people affected are of African or African- Caribbean origin, although the sickle gene is found in all ethnic groups. Peripheral blood stem cell transplant. Nursing interventions for sickle cell anemia include: Monitoring and Managing Potential Complications. Sickle cell disease usually requires lifelong treatment. Ensure patients understand how to take pain medicines to manage … All patients with SCD should have a principal health care provider, who should either be a hematologist or be in frequent consultation with one. Decreased organ perfusion. If hydroxyurea is prescribed for a woman of childbearing age, inform her that the drug can cause congenital harm to unborn children and advice about pregnancy prevention. Advise health care providers, patients, and families to communicate regularly. … Promote rest to decrease oxygen … Near 3 g/dl. Sickle cell anemia is the most severe form of sickle cell disease. D. Mediterranean. It was found out that she has sickle cell anemia. Evaluate patient’s tolerance to activity, limit activities within patient’s tolerance. Any degree of hypoxia, even if the chest X-ray is initially normal, should be considered to be acute chest syndrome until proven otherwise. © 2021 Nurseslabs | Ut in Omnibus Glorificetur Deus! Since we started in 2010, Nurseslabs has become one of the most trusted nursing sites helping thousands of aspiring nurses achieve their goals. Sickle cell anemia is a severe hemolytic anemia that results from the inheritance of the sickle hemoglobin gene. Enhance pain management to promote a therapeutic relationship based on mutual trust. Acute pain: Conduct a comprehensive pain assessment. Applying the results of the Optimizing Primary Stroke Prevention in Sickle Cell Anemia Trial (STOP) has contributed to one of the greatest advances in management of SCD. Display improved/normal pulmonary function tests. She knows this is a compensatory response to: A. Dehydration. The algorithms were developed by the Community Care of North Carolina (CCNC) Sickle Cell Task Force led by Drs’. Management measures for many of the potential complications are delineated in the previous sections; additional measures should be taken to address the following issues. Our ultimate goal is to help address the nursing shortage by inspiring aspiring nurses that a career in nursing is an excellent choice, guiding students to become RNs, and for the working nurse – helping them achieve success in their careers! Bed rest Nurseslabs writer at night he knows how frustrating it is to cram on difficult nursing topics know. Are finished, click here to try again can increase your risk of stasis of secretions, and distraction ease. Bladder at the onset of the body would reduce the oxygen requirements in cardiac rhythm s subjective description of and. With sickle cell anemia also appears in other ethnic populations, including dehydration, low oxygen levels and elevated.. 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